SPHINGO-LIPID SYNTHESIS

SPHINGO-LIPID SYNTHESIS:
AA SERINE+
FFA PALMITATE=
SPINGO-SINE+
FFA--> CERAMIDE:

DISEASE--> GRAY MATTER ONLY-->
IN NEURONES

Gal STAYS-->FABRY
XR 50y
META-CHROMATIC
LEUCO-DYSTROPHY

NO-MAN
P ICKs
P HOSPHATE
his nose with
hiSPHINGer
SPHINGomyelin

+MONO-SACCARIDE
G lu-CEREBROSIDE
G AUSHER
G LUCO-CEREBRO-SIDase\

S STAYS--> KRABBE

+OLIGO-SACCHARIDE-->
GANGLIO-SIDE
TAY-
SA X
HE X OS-AMIN-IDASE A